Cover image for Congenital Disorders of Erythropoiesis.
Congenital Disorders of Erythropoiesis.
Title:
Congenital Disorders of Erythropoiesis.
Author:
Symposium, CIBA Foundation.
ISBN:
9780470717875
Personal Author:
Edition:
1st ed.
Physical Description:
1 online resource (418 pages)
Series:
Novartis Foundation Symposia ; v.938

Novartis Foundation Symposia
Contents:
Congenital Disorders of Erythropoiesis -- Contents -- Chairman's opening remarks -- Cellular kinetics of erythropoiesis -- Discussion -- Regulation of fetal and adult erythropoiesis -- Discussion -- Embryonic erythropoiesis: some experimental systems -- Discussion -- Oxygen dissociation studies of red cells from chicken, mouse and human embryos -- Discussion -- General discussion I -- Diamond-Blackfan anaemia -- Discussion -- Fanconi anaemia -- Fanconi anaemia: cellular abnormalities and clinical predisposition to malignant disease -- Discussion of the two preceding papers -- Congenital dyserythropoietic anaemia type I : clinical and experimental aspects -- Discussion -- Congenital dyserythropoietic anaemia type I1 (Hempas) -- Discussion -- Congenital dyserythropoietic anaemias : electron microscopy -- Discussion -- Pathophysiology of the anaemia in thalassaemia -- Discussion -- The morphology and kinetics of erythropoiesis in homozygous β-thalassaemia -- Discussion -- The molecular defect in thalassaemia -- Discussion -- Cytogenetics of Fanconi anaemia and related chromosome disorders -- Discussion -- Fetal haemoglobin synthesis -- Discussion -- Regulation of globin gene expression -- Discussion -- General discussion II: Clinical management -- Conservative management -- Androgen therapy in aplastic anaemia in childhood -- Chelating agents -- Bone marrow transplants -- Genetic manipulation -- Antenatal diagnosis -- Concluding remarks -- lndex of contributors -- Subject index.
Local Note:
Electronic reproduction. Ann Arbor, Michigan : ProQuest Ebook Central, 2017. Available via World Wide Web. Access may be limited to ProQuest Ebook Central affiliated libraries.
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